Infantile myofibromatosis – a clinical and pathological diagnostic challenge
نویسندگان
چکیده
منابع مشابه
Infantile myofibromatosis*
Infantile myofibromatosis is a mesenchymal disorder characterized by the fibrous proliferation of the skin, bone, muscle and viscera. It is the most common fibrous tumor in childhood. We present a newborn with skin and bone disease without visceral involvement, who showed good response to vinblastine and methotrexate. Clinical features, etiology, diagnosis, and treatment are reviewed.
متن کاملInfantile Myofibromatosis
Infantile myofibromatosis (IMP) is a rare tumour with a wide spectrum of disease activity ra a solitarY cutaneous nodule through to a multicentric form ,vith widespread visceral involveluent. R is charactelised by its unique ability to spontaneously regress and has a typical histological appearance of a~tin-positivefibroblasts arranged in whorls or fascicles and vessels in a pericytomatous patt...
متن کاملInfantile myofibromatosis.
Infantile myofibromatosis (IMF) is a rare tumour with a wide spectrum of disease activity ranging from a solitary cutaneous nodule through to a multicentric form with widespread visceral involvement. It is characterised by its unique ability to spontaneously regress and has a typical histological appearance of actin-positive fibroblasts arranged in whorls or fascicles and vessels in a pericytom...
متن کاملMulticentric Infantile Myofibromatosis
We present a case of multicentric infantile myofibromatosis in a 3-month-old male infant who had multiple papular lesions on his extremities and trunk and a slowly growing and bulging mass on his left occipital area since birth. His general physical condition was good and psychomotor development was normal. The diagnosis was established by histopathological and immunohistochemical studies along...
متن کاملInfantile myofibromatosis: a cause of vertebra plana.
A 6-week-old boy was seen in the emergency department with progressive enlargement of head and neck masses. Bilateral periauricular masses had been present since birth and had undergone recent cervical extension. A mass of the right nasolabial fold had been present since 3 weeks of age. The lesions were asymptomatic and the infant was otherwise well. Computed tomography (CT) of the head and nec...
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ژورنال
عنوان ژورنال: Dermatology Online Journal
سال: 2017
ISSN: 1087-2108
DOI: 10.5070/d3234034632